Purpose or Case Report: The inner ear anomalies are a complex group of disorders, the radiologic findings of which may be difficult to interpret. This exhibit details the basic embryology of inner ear with stress on correlation of timing of insult or arrest of development to patho-morphology, the classification schema of inner ear anomalies and various salient features aiding in accurate diagnosis.
Methods & Materials: We commence by describing the relevant embryology of inner ear with stress on implications of timing of insult on patho-morphology. The various pathologies we will be discussing include: 1. Anomalies of semicircular canal: CHARGE syndrome, semicircular canal - vestibule globular anomaly, semicircular canal dysplasia - Waardenburg syndrome, dehiscence of superior semicircular canal (Minor's syndrome), 2. Anomalies of cochlea: complete labyrinthine aplasia, cochlear aplasia, common cavity malformation, incomplete partition type I, cochlear hypoplasia, incomplete partition type II, 3. Miscellaneous: oval window atresia, stapes gusher syndrome, stenosis of IAC, and Branchio-oto-renal syndrome.

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