Purpose or Case Report: Show the imaging findings in a series of 4 OHVIRA syndrome, cases reported, in our hospital in a period of 10 years (May 2009 and May2019).
Methods & Materials: Femenines <15yo, with pelvic ultrasound and MRI, between May 2009 and May 2019, that reveals signs of complete uterine duplication, including the body and cervical region, presence of a vaginal septum with obstructed hemivagina and renal agenesia.
Results: 4 femenine patients with 10, 11, 13 and 14 years old with complete uterine duplication.
3 patients with right renal agenesia, 1 patient with left renal agenesia.
3 patients with right obstructed hemivagina, 1 patiente with left obstructed hemivagina.
Conclusions: Due to the complexity of the manifestations, the diagnosis of Müllerian malformations requires more than one imaging method.
MRI is the most appropriate imaging method, with a sensitivity and accuracy close to 100%, providing great uterine anatomical detail.
The recognition and early surgical treatment of this rare entity is important to avoid symptoms, preserve fertility and avoid complications.