Purpose or Case Report: 12 year old female presented with history of ureteral re-implantation and severe pelvic pain for a month. Pelvic ultrasound showed a bi-lobed hypoechoic mass in the pelvis markedly distended with internal intermediate and low level echoes and septations suggestive of hematometrocolpos thought to be secondary to imperforate hymen. Subsequent MRI evaluation of the pelvis demonstrated a complete septate uterus with longitudinal vaginal septum, atresia of the lower 1/3 of the vagina, and hematocolpos. The patient was placed on Lupron and referred for reconstructive surgery.
Methods & Materials: Complete septate uterus and longitudinal vaginal septum combined with atresia of the lower third of the vagina is a rare congenital anomaly representing a combination of a Mullerian duct anomaly and failure of the primitive urogenital sinus to develop.
Results:
Conclusions: Through this case we will discuss the embryology and imaging findings of septate uterus and vagina and vaginal atresia with review of the literature.