Purpose or Case Report: The incidence of upper genitourinary anomalies in children has been reported up to 4-6% and the association of cryptorchidism, hypospadias, double collecting system or fused kidney with Wilms’ tumor is well known. Horseshoe kidney is a rare anomaly of fusion occurring between 4^th and 6^th weeks of gestation. The association of Wilms’ tumor with horseshoe kidney is uncommon, with limited cases described. The incidence varies from 0.4% to 0.9% of all Wilms’ tumor. Rare variants of Wilms’ tumor like extrarenal teratoid tumor have also been described in children with horseshoe kidney. We describe two cases of Wilms’ tumor arising from horseshoe kidney, detected on US and later confirmed on CE-CT with low-dose imaging protocol. Both cases underwent surgical resection of the abnormal kidney and the diagnosis of Wilms’tumor was confirmed on microscopic examination of the excised tumor. In presence of kidney abonormalities imaging surveillance and follow-up evaluation is mandatory in order to grant an early detection of neoplastic evolution.
In our experience, multislice CT allows complete preoperative evaluation of this rare condition mainly using multiplanar reconstructions and may facilitate surgery.
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