Purpose or Case Report: The pediatric population is not immune to the various types of cancer encountered by the adult population in terms of the organs and organ systems affected. Despite advances in treatments and detection, cancer is still the number 2 cause of death within the pediatric population. The types of tumors encountered in the younger population are often composed of more uniquely immature cellular lineages and only a small percentage have preventable causes. The goal of our single institution presentation is to provide the interested viewer with a comprehensive review of several uniquely encountered immature pediatric tumors. Our presentation will include imaging examples utilizing multiple modalities demonstrating examples of pancreaticoblastoma , immature lipoblastoma, neuroblastoma, hepatoblastoma, a case of biopsy confirmed small cell undifferentiated renal rhabdoid tumor, and a unique case of pleuropulmonary blastoma. Explanations pertaining to the key imaging features of each entity as reported in the literature will be provided to supplement the case examples from our institution.
Methods & Materials: Our exhibit includes a comprehensive case-based review of the pertinent multimodal imaging findings of several rare congenital pediatric malignancies. Our review will include imaging examples and descriptions of pancreaticoblastoma, lipoblastoma, pleuropulmonary blastoma, hepatoblastoma, small cell undifferentiated renal rhabdoid tumor, and neuroblastoma.
Results:
We provide an educational radiographic review of multiple rare congenital pediatric malignancies. We use a multimodal approach to evaluating each lesion and its extent, utilizing CT, MR, ultrasound and PET imaging.
Conclusions: Congenital Pediatric tumors present with unique radiographic features resulting in a complicated constellation of findings. The radiologist's role in accurate diagnosis of these lesions and understanding of their imaging characteristics plays a crucial role in patient care and management.