Main Logo
Logo

Society for Pediatric Radiology – Poster Archive

  292
  0
  0
 
 


Final ID: Poster #: CR-012

A Case Study of Obstructed Hemi-vagina with Ipsilateral Renal Agenesis (OHVIRA), A Rare Müllerian Duct Anomaly

Purpose or Case Report:
Imaging findings are diagnostic of obstructed hemi-vagina with ipsilateral renal agenesis (OHVIRA). This is a rare condition consisting of a triad of uterine didelphys (a type III Müllerian duct anomaly), hematocolpos, and ipsilateral renal agenesis. If any of these three features are absent, the diagnosis of OHVIRA is excluded. Clinical presentation is typically 2-12 months post menarche. Though rare pre-pubertal onset has been documented secondary to maternal hormonal influence, the mean age of presentation is 17 years old. Symptoms are typically non-specific including dysmenorrhea and a palpable pelvic mass.

Complications:
Acute complications of OHVIRA include primarily infection of retained blood products resulting in pyohematocolpos or pyosalpinx. Rarely pelviperitonitis can occur if hematocolpos progresses to a hematosalpinx which ruptures. Long term complications include endometriosis, thought secondary to retrograde flow of blood products, which can lead to development of pelvic adhesions. Infertility issues are thought largely to be secondary to endometriosis and/or infection more so than uterine didelphys. Additional obstetric complications are greater in patients without surgical correction and most patients who carry a pregnancy to term have no increased difficulty.

Treatment:
Surgical correction with vaginal septectomy or division is the first line treatment for OHVIRA. If surgical correction is achieved early, the risk of complications including infertility are greatly diminished.
Methods & Materials: Gray-scale ultrasound of the pelvis shows the uterus with a large distended and fluid filled vagina. MRI of the pelvis demonstrates uterine didelphys, an enlarged and dilated hemi-vagina containing T1 bright blood products consistent with hematocolpos, and a second nondilated hemi-vagina. MRI of the lower abdomen and pelvis displays an absent left renal fossa and solitary right kidney.
Results:
Conclusions:
  • Smith, Jennifer  ( University of New Mexico Health Sciences Center , Albuquerque , New Mexico , United States )
  • Richards, Allyson  ( University of New Mexico Health Sciences Center , Albuquerque , New Mexico , United States )
  • Revels, Jonathan  ( University of New Mexico Health Sciences Center , Albuquerque , New Mexico , United States )
Session Info:

Posters - Case Report

GU

SPR Posters - Case Reports

More abstracts on this topic:
Where are We Exactly?: Navigating the Complex Roadmap of Müllerian Duct Anomalies

Myers Ross, Li Tianyang, Wu Jennifer, Sadowsky David, Paul Mary, Gerard Perry, Brudnicki Adele, Lecompte Lesli

A Rare Congenital Urogenital Anomaly: Case Report in a University Hospital in Chile.

Chang Santos Santiago, Garcia Cristian, De Barbieri Florencia

Preview
Poster____CR-012.pdf
You have to be authorized to contact abstract author. Please, Login or Signup.

Please note that this is a separate login, not connected with your credentials used for the SPR main website.

Not Available

Comments

We encourage you to join the discussion by posting your comments and questions below.

Presenters will be notified of your post so that they can respond as appropriate.

This discussion platform is provided to foster engagement, and stimulate conversation and knowledge sharing.

Please click here to review the full terms and conditions for engaging in the discussion, including refraining from product promotion and non-constructive feedback.

 

You have to be authorized to post a comment. Please, Login or Signup.

Please note that this is a separate login, not connected with your credentials used for the SPR main website.


   Rate this abstract  (Maximum characters: 500)