Not Available
Society for Pediatric Radiology – Poster Archive
Final ID: Poster #: EDU-019
Review of Congenital Renal Anomalies: A Case of Crossed Fused Renal Ectopia
Purpose or Case Report: Learning Objectives:
Review normal kidney development and embryology
Understand spectrum of renal fusion abnormalities, associated genitourinary abnormalities, and their clinical manifestations
Recognize imaging findings and important associations
Kidney Development and Abnormalities:
The metanephric blastema becomes the functioning kidney and the ureteric bud develops into the ureters and upper collecting system. Typical kidney development begins at 4 weeks gestation. Over 4-7 weeks gestations, the developing kidneys rise from the sacrum to the abdomen moving apart from each other and rotating medially with final positioning at week 9.
Renal positioning defects include malrotation which is abnormal rotation of the kidney along its long axis. The hilum often faces anteriorly, as the kidney fails to medially rotate during ascent.
Ectopic kidneys are position defects where the kidneys are not located in the renal fossa. Renal ectopia can be simple, wherein the kidney remains ipsilateral, or crossed, wherein the kidney is located contralateral to the distal ureter insertion. Pelvic kidney is the most common simple ectopia. Ectopic kidneys may coexist with fusion defects. Associated symptoms include vesicoureteral reflux, increased urinary tract infections, and renal calculi formation.
The horseshoe kidney is the most common congenital partial renal fusion abnormality (1/400 live births with male predilection).
Case Report:
Our case report had a prenatal diagnosis of absent left kidney and postnatal diagnosis of imperforate anus. Ultrasound revealed left to right crossed fused renal ectopia. Voiding cystourethrogram demonstrated additional abnormalities in the genitourinary tract, including a fistulous connection between the bladder and uterine segment/vagina and bifid appearance of the uterus with bilateral grade II vesicoureteral reflux. MRI redemonstrated left-to-right crossed fused renal ectopia and vesicovaginal/rectovaginal fistulas.
Conclusion
Cross fused renal ectopia is part of a spectrum of congenital genitourinary abnormalities and are common in prenatal assessment.
Methods & Materials:
Results:
Conclusions:
Review normal kidney development and embryology
Understand spectrum of renal fusion abnormalities, associated genitourinary abnormalities, and their clinical manifestations
Recognize imaging findings and important associations
Kidney Development and Abnormalities:
The metanephric blastema becomes the functioning kidney and the ureteric bud develops into the ureters and upper collecting system. Typical kidney development begins at 4 weeks gestation. Over 4-7 weeks gestations, the developing kidneys rise from the sacrum to the abdomen moving apart from each other and rotating medially with final positioning at week 9.
Renal positioning defects include malrotation which is abnormal rotation of the kidney along its long axis. The hilum often faces anteriorly, as the kidney fails to medially rotate during ascent.
Ectopic kidneys are position defects where the kidneys are not located in the renal fossa. Renal ectopia can be simple, wherein the kidney remains ipsilateral, or crossed, wherein the kidney is located contralateral to the distal ureter insertion. Pelvic kidney is the most common simple ectopia. Ectopic kidneys may coexist with fusion defects. Associated symptoms include vesicoureteral reflux, increased urinary tract infections, and renal calculi formation.
The horseshoe kidney is the most common congenital partial renal fusion abnormality (1/400 live births with male predilection).
Case Report:
Our case report had a prenatal diagnosis of absent left kidney and postnatal diagnosis of imperforate anus. Ultrasound revealed left to right crossed fused renal ectopia. Voiding cystourethrogram demonstrated additional abnormalities in the genitourinary tract, including a fistulous connection between the bladder and uterine segment/vagina and bifid appearance of the uterus with bilateral grade II vesicoureteral reflux. MRI redemonstrated left-to-right crossed fused renal ectopia and vesicovaginal/rectovaginal fistulas.
Conclusion
Cross fused renal ectopia is part of a spectrum of congenital genitourinary abnormalities and are common in prenatal assessment.
Methods & Materials:
Results:
Conclusions:
More abstracts on this topic:
"Pancake" Kidney: A Rare Subtype of a Rare Congenital Anomaly
Farhat Ahmed, Huang Pauline, Servaes Sabah, Hailemichael Eyassu
Ultrasound Shearwave Elastography in Pediatric Renal TransplantsRiemann Monique, Bailey Smita, Angadi Siddhartha, Biyyam Deepa, Turman Martin
Poster____EDU-019.pdf
Comments
We encourage you to join the discussion by posting your comments and questions below.
Presenters will be notified of your post so that they can respond as appropriate.
This discussion platform is provided to foster engagement, and stimulate conversation and knowledge sharing.
Please click here to review the full terms and conditions for engaging in the discussion, including refraining from product promotion and non-constructive feedback.
You have to be authorized to post a comment. Please,
Login or
Signup.
Please note that this is a separate login, not connected with your credentials used for the SPR main website.
Rate this abstract
(Maximum characters: 500)
Please note that this is a separate login, not connected with your credentials used for the SPR main website.