Purpose or Case Report: 1) To review the embryology of the temporal bone with emphasis of the external and middle ear.
2) To review the detailed cross sectional CT anatomy of the temporal bone.
3) To describe the cross-sectional imaging findings of common and uncommon pathologies of congenital conductive hearing loss.
Methods & Materials: Retrospective search of the Radiology PACS system at Tertiary Level Children Hospital was performed using keyword “Congenital”, “Conductive Hearing Loss”. Representative cases were identified and included in this exhibit.
The exhibit begins with a review of the embryology and detailed cross-sectional anatomy of the temporal bone. This is followed by a detailed discussion of imaging and clinical findings of common and uncommon pathologies of congenital conductive hearing loss.
Then the audience has the opportunity to apply the knowledge toward diagnosing pathologies of congenital conductive hearing loss via an interactive case-based approach.
Results: Various common and uncommon pathology of the external and middle ear structures were encountered and included in this exhibit including, not limited to external auditory canal atresia, oval window atresia, round window atresia, congenital ossicular anomalies and fixation, congenital cholesteatoma etc.
Conclusions: Knowledge of the embryology, cross sectional anatomy and imaging characteristics of various common and uncommon pathologies of Congenital Conductive Hearing Loss will allow an accurate timely diagnosis, appropriate treatment selection and surgical approach of these lesions.