Purpose or Case Report: Congenital extrahepatic portosystemic shunt (CEPS), also known as Abernethy malformation, is a rare congenital vascular abnormality in which portosplenomesenteric blood drains directly into the systemic venous system, thus bypassing the liver via an extrahepatic shunt. CEPS classification is based on the shunt anatomy and presence of an intrahepatic portal venous supply, which affects the form of definitive treatment available. Complications can arise due to the metabolic abnormalities and altered hemodynamics brought about by the shunt. Imaging plays a crucial role in the initial diagnosis and surgical planning, as well as the identification and monitoring of complications.
The purpose of this educational exhibit is to review the CEPS embryological origins, classification system and complications through various case examples across different imaging modalities (ultrasound, CT, MRI and angiography).
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