Lee Simon,  Krishnamurthy Rajesh,  Krishnamurthy Ramkumar,  Johnston Thomas,  Hor Kan

Final Pr. ID: Poster #: SCI-009

Duchenne muscular dystrophy (DMD) is a myopathy with a natural history of progressive cardiomyopathy and vasogenic edema, fatty infiltration, and myocardial fibrosis. We recently identified a group of patients with DMD who presented with acute onset of chest pain (ACP), troponin leak (TL), and new late gadolinium enhancement (LGE), similar in presentation to acute viral myocarditis (AM). It is unclear if these patients have suffered an episode of AM or if this is a different disease process. Given the presumed acute myocardial necrosis in both processes, we hypothesize that native T1 and T2 values would be elevated in AM and DMD patients with ACP compared to asymptomatic DMD patients. Read More

Authors:  Lee Simon , Krishnamurthy Rajesh , Krishnamurthy Ramkumar , Johnston Thomas , Hor Kan

Keywords:  Parametric Mapping, Cardiomyopathy

Sharma Priya,  Rajderkar Dhanashree

Final Pr. ID: Poster #: EDU-114

Learning Objectives: This educational exhibit will review glycogen storage diseases and the imaging findings of these disease processes using a multimodality approach. We will also review complications and discuss the treatment and role of imaging as a measure of treatment response. Read More

Authors:  Sharma Priya , Rajderkar Dhanashree

Keywords:  Glycogen Storage Diseases, Hepatic Adenoma, Hepatocellular Carcinoma, Cardiomyopathy, GSD

Zucker Evan

Final Pr. ID: Poster #: EDU-093

Cardiomyopathy is rare in children but associated with significant morbidity and mortality when symptomatic. It also comprises a large proportion of cardiac MR imaging referrals in typical pediatric radiology practice. The purpose of this educational exhibit is to review the major types of cardiomyopathy in children, focusing on cardiac MRI. Read More

Authors:  Zucker Evan

Keywords:  Cardiomyopathy, Cardiac, MRI, Pediatric, Late gadolinium enhancement

Johnston Thomas,  Lee Simon,  Krishnamurthy Ramkumar,  Krishnamurthy Rajesh,  Hor Kan

Final Pr. ID: Poster #: SCI-010

Cardiomyopathy is the leading cause of mortality for Becker Muscular Dystrophy (BMD).Risk stratification is challenging due to the wide variation of cardiomyopathy onset, progression, and severity; with cardiomyopathy developing independent of skeletal myopathy progression. Current guidelines recommend “complete cardiac evaluation” at ten years of age, but do not specify the type of imaging modality. We have been performing cardiac magnetic resonance imaging (CMR) routinely by 10 years of age. We sought to determine the progression of BMD cardiomyopathy during the adolescent years among patients who have evidence of fibrosis by late gadolinium enhancement(LGE). Read More

Authors:  Johnston Thomas , Lee Simon , Krishnamurthy Ramkumar , Krishnamurthy Rajesh , Hor Kan

Keywords:  Cardiomyopathy, LGE