Shannon Leann,  Singh Sudha

Final Pr. ID: Poster #: EDU-085

With research pushing ever onward, it is often difficult to keep pace with the dynamic landscape of pediatric abdominal tumors and their classification systems. However, it is imperative that we, as radiologists, remain vigilant of these changes, as our initial and follow-up imaging assessments often have the potential to drive clinical intervention in widely differing directions.

In this educational poster, we will review the most up-to-date risk stratification and staging criteria for neuroblastoma, hepatoblastoma, and Wilms tumor in order to:

1. Educate about the most recent criteria for categorizing pediatric abdominal tumors such as neuroblastoma, hepatoblastoma, and Wilms tumor.

2. Provide imaging examples of these pediatric abdominal tumors and describe how the above-mentioned criteria might change radiology reports and patient management.

3. Encourage accurate risk stratification of these tumors so that radiologists are better equipped to assist in directing appropriate patient care. Read More

Authors:  Shannon Leann , Singh Sudha

Keywords:  neuroblastoma, hepatoblastoma, Wilms

Miyazaki Osamu,  Oguma Eiji,  Nishikawa Masanori,  Tanami Yutaka,  Kitami Masahiro,  Hosokawa Takahiro

Final Pr. ID: Poster #: SCI-026

To assess the size and number of pulmonary lesions in patients with hepatoblastoma
Diagnostic criteria of the PRETEXT (Pretreatment Extent of Disease) staging system for hepatoblastoma states that pulmonary lesions are judged to be metastases if there is one nodule greater than 10mm in diameter, or if among several nodules at least one is greater than 5mm in diameter. Read More

Authors:  Miyazaki Osamu , Oguma Eiji , Nishikawa Masanori , Tanami Yutaka , Kitami Masahiro , Hosokawa Takahiro

Keywords:  hepatoblastoma, lung metastasis, chest CT

Hall Chase,  Germaine Colton,  Richards Allyson,  Tocchio Shannon

Final Pr. ID: Poster #: EDU-046

Overview:
Although rare, with only about 100 de novo cases reported a year, hepatoblastoma is the most common primary pediatric liver tumor in children under 3 years of age. The imaging findings of hepatoblastoma can be difficult to identify, especially for trainees, since not many radiologists have the opportunity to diagnose patients with this condition. Additionally, given the high rate of metastases, often to the skeletal system, at the time of diagnosis there is overlap with findings of non-accidental trauma. Treatment for hepatoblastoma requires specialized teams and prompt diagnosis with appropriate referrals resulting in improved management and prognosis. In this educational exhibit we review a de novo case of hepatoblastoma diagnosed at The University of New Mexico, with a focus on essential ultrasound, CT and MRI findings. Additionally, we will discuss associated gene mutations and congenital disorders, common sites of metastasis and how to use the PRETEXT method to risk stratify and guide management.

Outline:
Overview of hepatoblastoma
Review gene mutations and congenital disorders associated with hepatoblastoma
Review important findings of hepatoblastoma on ultrasound, CT and MRI, using unique images obtained at the University of New Mexico
Discuss common sites of metastasis and how osseous metastases can raise concerns non-accidental trauma
Checklist of how to use PRETEXT and brief review of treatment options

Goals:
Improve understanding of hepatoblastoma
Provide radiologist, especially trainees, with the tools necessary to recognize hepatoblastoma across multiple imaging modalities
Discuss how radiologists can provide focused management recommendations for treatment teams Read More

Authors:  Hall Chase , Germaine Colton , Richards Allyson , Tocchio Shannon

Keywords:  Hepatoblastoma, Rare Neoplasms, MRI

Yadava Rohtas

Final Pr. ID: Poster #: SCI-016

To see the profile of various Pediatric Abdominal Mass Lesions on MDCT and to evaluate the diagnostic accuracy of MDCT in detection and characterization of various Pediatric Abdominal Mass Lesions. Read More

Authors:  Yadava Rohtas

Keywords:  Hepatoblastoma, Ewing Sarcoma, Adrenal Pheochromocytoma

Maller Vijetha,  Arora Anurag,  Boulden Thomas,  Choudhri Asim

Final Pr. ID: Poster #: CR-013

A newborn male child with antenatal diagnosis of left facial mass presumably hemangioma, presented for postnatal ultrasound. Ultrasound of the left face and neck, showed a large homogenous mass measuring 5x7x4 cm arising from the inferior aspect of the superficial lobe and entire deep lobe of the parotid gland extending over the angle of mandible to the left parapharyngeal space. On MRI the mass was heterogenously enhancing with low signal intensity on T1 and intermediate signal on T2 weighted imaging. The mass was also extending into the left masticator, sublingual, and submandibular spaces. The neonate also had a right upper abdominal swelling, and an ultrasound abdomen detected heterogeneously hypo to hyperechoic mass in the segment 4 of liver. On triple phase computed tomography, the mass showed early peripheral arterial enhancement and heterogeneous enhancement in portal and venous phase. On magnetic resonance imaging, the mass was hyperintense to liver on T2-weigthed imaging with restricted diffusion and heterogenous enhancement less than the background liver on all phases. Biopsy result of the left facial mass was sialoblastoma and that of liver was hepatoblastoma. Alpha fetoprotein was also elevated. Wide margin surgical resection of sialoblastoma and left lobe hepatectomy was performed followed by chemotherapy.

Sialoblastoma is a rare congenital tumor of the salivary glands, mainly arising from the parotid gland, which is locally aggressive and potentially malignant. A total of approximately 40 cases of congenital sialoblastoma has been reported. Neonatal hepatoblastomas comprises 10% of pediatric hepatoblastomas. An association of sialoblastoma and centromere division has been reported, which in turn is associated with embryonal tumors. There have been only two reported cases of concomitant sialoblastoma and hepatoblastoma. Further research with genetic analysis is required to document association of these two embryonal tumors. The current management of these tumors is complete surgical resection followed by chemotherapy. Read More

Authors:  Maller Vijetha , Arora Anurag , Boulden Thomas , Choudhri Asim

Keywords:  Sialoblastoma, Hepatoblastoma

Guo Chen,  Zhong Yumin,  Zhou Ying,  Hu Li-wei

Final Pr. ID: Poster #: SCI-018

To apply the Couinaud’ system of segmentation and PRETEXT staging system of the liver to the tumor staging, combined with MSCT for evaluate the effectiveness in pre or post therapy of hepatoblatoma. Read More

Authors:  Guo Chen , Zhong Yumin , Zhou Ying , Hu Li-wei

Keywords:  Hepatoblastoma, PRETEXT staging system, Liver