Shah Summit,  Bates D. Gregory,  Levitt Marc,  Wood Richard,  Thompson Benjamin

Final Pr. ID: Poster #: EDU-111

1. To demonstrate the appropriate technique for performing a contrast enema in symptomatic post-surgical Hirschsprung disease (HD).
2. To review the three major surgical procedures used for the primary treatment of HD, their complications, and imaging manifestations. Read More

Authors:  Shah Summit , Bates D. Gregory , Levitt Marc , Wood Richard , Thompson Benjamin

Keywords:  Hirschsprung, Anorectal, Enema

Martin Camden,  Cassella Katharyn,  Johnstone Lindsey,  Leschied Jessica

Final Pr. ID: Poster #: EDU-028

Anorectal malformations (ARMs) are a heterogenous group of congenital anomalies involving the distal rectum and anus that are often associated with other anomalies. Neonates with ARMs may be identified at birth or prenatally and, upon delivery, receive a myriad of imaging tests to characterize the type of ARM and associated anomalies. Recent literature supports the use of transperineal ultrasound in the initial assessment of neonates with ARMs, with the Society of Pediatric Radiology recommending its use in the imaging algorithm for ARMs. Transperineal ultrasound, if adequately performed, allows evaluation of the location of the distal rectal pouch and the anatomy and location of any rectourogenital fistulas. In this educational poster, we review the clinical presentation and classification ARMs and discuss the role of transperineal ultrasound in the initial assessment of cases. We then describe common sonographic findings of ARMs on transperineal ultrasound using examples from our own institution. Our goal is to familiarize pediatric radiologists with this heterogenous group of congenital anomalies and the clinical utility of transperineal ultrasound in characterizing this pathology. Read More

Authors:  Martin Camden , Cassella Katharyn , Johnstone Lindsey , Leschied Jessica

Keywords:  Gastrointestinal, Anorectal, Ultrasound

Wepking Kelly,  Gill Kara,  Riedesel Erica

Final Pr. ID: Poster #: CR-068

Currarino’s Syndrome (CS) is a unique form of caudal regression syndrome characterized by triad of sacral dysplasia, anorectal malformation, and presacral mass. Additional congenital malformations of the genitourinary tract and spine may be present.

Currarino's Syndrome has a variety of clinical presentations - from asymptomatic to severe chronic constipation - depending on associated malformations. Early identification and adequate treatment prevents eventual serious complications.

Plain radiograph of the sacrum is the first diagnostic step. Ultrasound or pelvic/spinal MRI is used to better evaluate for presacral mass. Fluoroscopic enema studies may be used for further evaluation of anorectal malformation. Additional imaging of the GU tract with US and VCUG is suggested due to risk for associated GU anomaly or vesicoureteral reflux.

We present two cases of Currarino’s Syndrome which demonstrate classic imaging findings on plain film radiograph, ultrasound, and MRI.

Case 1 presented in infancy with severe chronic constipation. Abdominal radiograph demonstrated classic "scimitar" sacrum. Fluoroscopic enema demonstrated high grade anal stenosis. US and MRI of the spine and sacrum revealed large anterior sacral meningocele.

Case 2 presented at birth with imperforate anus. Abdominal radiograph demonstrated classic "scimitar" sacrum. MRI of the spine and sacrum revealed small anterior sacral meningocele. Additional GU anomalies were discovered including vesicoureteral reflux and uterine didelphis. Read More

Authors:  Wepking Kelly , Gill Kara , Riedesel Erica

Keywords:  Currarino's Triad, Sacral dysplasia, Presacral mass, Anorectal malformation, Case Report

Jain Nikshita,  Haider Seemab,  Boag Graham,  Bhandal Samarjeet

Final Pr. ID: Poster #: EDU-019

Anorectal malformations are a fairly common group of congenital anomalies presenting at birth and often as part of a syndrome, with various other associated entities. The purpose of this article is to detail the role of imaging in the evaluation of the anomalies and provide a simple approach to reporting that will provide all the necessary anatomic details to the surgeons for best possible surgical and functional outcome. Read More

Authors:  Jain Nikshita , Haider Seemab , Boag Graham , Bhandal Samarjeet

Keywords:  Anorectal, congenital, malformations