Kaposiform hemangioendotheliomas (KHE) are rare, locally aggressive vascular neoplasms. KHE most commonly arise from the extremities and less frequently the trunk and head and neck regions. Kasabach-Merritt phenomenon complicates 70% of cases. Three cases of KHE underwent prenatal evaluation and postnatal management at our center. We report the imaging findings that may allow for improved prenatal diagnosis. Case 1: 31-year-old G4P2 evaluated for cervicofacial mass at 24 weeks 5 days. Fetal ultrasound demonstrated a large, infiltrative, predominately solid, mildly heterogeneous mass with a volume of 62 mL. No calcifications or lesion hypervascularity were present. Same day MRI confirmed an infiltrative, predominately solid mass with mild heterogenous T2 signal and no internal flow voids. Repeat MRI at 34 weeks 5 days revealed increased lesion heterogeneity and internal flow voids. US at 36 weeks 3 days demonstrated a volume of 525 mL and lesion hypervascularity. Delivery was at 36 weeks 5 days by EXIT procedure. Kasabach-Merritt phenomenon developed, and postnatal biopsy was consistent with KHE. Case 2: 35-year-old G2P1 evaluated for cervical mass at 40 weeks 4 days. Fetal ultrasound demonstrated a large, infiltrative predominately solid, mildly heterogeneous mass with a volume of 180 mL. Calcifications and hypervascularity were present. Fetal MRI was not performed. Delivery the next day was by cesarean section. Kasabach-Merritt phenomenon developed. Postnatal biopsy was consistent with KHE. Case 3: 30-year-old G1P0 evaluated for cervical mass at 38 weeks 1 day. Fetal ultrasound demonstrated a large, predominately solid, heterogeneous mass with a volume of 242 mL. Calcifications and hypervascularity were present. Same day fetal MRI confirmed an infiltrative, predominately solid mass with heterogeneous T2 signal and internal flow voids. Delivery was at 38 weeks 3 days by cesarean section. Kasabach-Merritt phenomenon developed, and postnatal MRI and clinical findings were consistent with KHE. Read More

Meeting name: SPR 2022 Annual Meeting & Postgraduate Course , 2022

Authors: Huynh Minh-huy, Didier Ryne, Feygin Tamara, Paidas Teefey Christina, Coleman Beverly, Oliver Edward

Keywords: Kaposiform hemangioendothelioma, cervical masses

Clinical signs of the Neonatal Lymphatic Flow Disorder (NLFD) are a combination of the congenital chylothorax, chylous ascites and body edema. It can present as neonatal chylothorax (NC), neonatal chylous ascites, or congenital lymphatic dysplasia (CLD). The prenatal appearance of lymphangiectasia has been described as nutmeg lung. The purpose of this study is to describe prenatal and postnatal imaging features and outcomes of neonates with NLFD. Read More

Meeting name: SPR 2017 Annual Meeting & Categorical Course , 2017

Authors: Biko David, Johnstone Jordan, Dori Yoav, Itkin Maxim, Oliver Edward, Victoria Teresa

Keywords: lymphatic imaging, nutmeg lung, neonatal lymphatic flow disorder

To report the prenatal ultrasound (US) and magnetic resonance imaging (MRI) findings in a prenatally diagnosed case of closed (i.e. skin-covered) cloacal exstrophy. Read More

Meeting name: SPR 2020 Annual Meeting & Postgraduate Course , 2020

Authors: Oliver Edward, Gitman Olga, Gebb Juliana, Weiss Dana, Canning Douglas, Hedrick Holly, Howell Lori, Coleman Beverly

Keywords: Abdominal Wall Defect, Prenatal Imaging