Pulmonary sequestration is a rare lung malformation characterized by non-functioning pulmonary parenchyma that lacks normal communication with the tracheobronchial tree and receives its blood supply aberrantly from the systemic circulation. Traditionally classified into extralobar (ELS) and intralobar (ILS) subtypes, the disease exists on a spectrum defined by variations in arterial supply and venous drainage. Complications include congestive heart failure related to systemic-to-pulmonary shunting, torsion, spontaneous hemorrhage, infection, and potential malignant degeneration, necessitating early diagnosis and surgical resection in most instances. Imaging plays a crucial role in preoperative planning by accurately identifying arterial and venous supply, subsequently reducing the risk of complications such as intraoperative hemorrhage and unplanned surgical approaches. The purpose of this exhibit is to: -Define the pulmonary sequestration spectrum of disease, including current theories on etiology, incidence, presentation, and complications. -Discuss the benefits and advantages of currently used imaging modalities, in addition to typical imaging characteristics of pulmonary sequestration and common differential diagnoses. -Emphasize the importance of a standardized reporting style for lung malformations, particularly one that focuses on the identification of vascular supply, and provide an example of such a reporting approach. Read More

Meeting name: SPR 2025 Annual Meeting , 2025

Authors: Vissing Dana, Thompson Matthew

Keywords: Sequestration, Congenital, Imaging