Congenital lung malformations are a heterogeneous group of developmental disorders whose etiology is not well stablished. Since they represent a spectrum of anomalies, diverse imaging appearance and clinical manifestations can be found. Although rare, their clinical importance is remarkable. Some of them can be a source of important morbidity and mortality in infants and children. Others, however, remain asymptomatic and may be incidentally detected in adulthood. Nowadays, these malformations are usually diagnosed in utero by prenatal imaging. In order to optimize diagnostic accuracy and disease management, it is imperative for radiologists to be familiar with the imaging characteristics of each lesion and the proper methods employed in their evaluation. The purpose of this exhibit is: - To describe the postnatal radiological appearance of some congenital lung diseases on conventional radiography, ultrasound (when available) and cross-sectional imaging methods; - To conduct a brief review of the literature regarding etiology, epidemiology, clinical features and adequate diagnostic approach; - To highlight the key imaging findings of each abnormality and their differential diagnoses; - To briefly discuss management and follow-up of each condition. Illustrative cases from our Radiology Department will be used to demonstrate the following entities: 1. Parenchymal anomalies: - Lung hypoplasia; - Congenital bronchial atresia; - Congenital lobar emphysema; - Congenital pulmonary airway malformation (previously known as congenital cystic adenomatoid malformation); - Pulmonary bronchogenic cysts; - Tracheal bronchus; - Accessory cardiac bronchus. 2. Vascular anomalies: - Interruption of a main pulmonary artery; - Pulmonary artery stenosis; - Anomalous pulmonary venous drainage. 3. Combined parenchymal and vascular anomalies: - Bronchopulmonary sequestration; - Hypogenetic lung (scimitar) syndrome. Read More

Meeting name: SPR 2020 Annual Meeting & Postgraduate Course , 2020

Authors: Defendi Larissa, Yokoo Patricia, Shoji Hamilton, Balancin Marcelo, Chate Rodrigo

Keywords: Congenital, Vascular, Lung

Small Round Blue Cell Tumors comprises a group of highly aggressive malignant tumors with overlapping morphological pattern and immunophenotypic characteristics. They represent a challenge for surgical pathologists, as they require a broad panel of antibodies, mostly not used in the routine work of most pathology laboratories. In the required multidisciplinary approach, radiologists play a vital role in narrowing the diagnosis. The aim of the presentation is to describe the imaging appearance of several Small Round Blue Cell Tumors, mainly in Magnetic Resonance (MR). Teaching cases from our Radiology Department will be used to illustrate the following: a) Ewing sarcoma; b) Peripheral primitive neuroectodermal tumor; c) Neuroblastoma; d) Wilms tumor; e) Hepatoblastoma; f) Embryonal Rhabdomyosarcoma; g) Medulloblastoma; h) Pineoblastoma; i) Retinoblastoma; j) Central Nervous System primitive neuroectodermal tumor; k) Neuroepithelioma; l) Desmoplastic small round cell tumor. Read More

Meeting name: SPR 2022 Annual Meeting & Postgraduate Course , 2022

Authors: Defendi Larissa De Andrade, Balancin Marcelo, Tostes Rodrigo De Oliveira, Rodriguez Larry Marden Rabindranath Alpaca, Regacini Rodrigo, Lederman Henrique

Keywords: Small Round Blue Cell Tumors