Small Round Blue Cell Tumors comprises a group of highly aggressive malignant tumors with overlapping morphological pattern and immunophenotypic characteristics. They represent a challenge for surgical pathologists, as they require a broad panel of antibodies, mostly not used in the routine work of most pathology laboratories. In the required multidisciplinary approach, radiologists play a vital role in narrowing the diagnosis. The aim of the presentation is to describe the imaging appearance of several Small Round Blue Cell Tumors, mainly in Magnetic Resonance (MR). Teaching cases from our Radiology Department will be used to illustrate the following: a) Ewing sarcoma; b) Peripheral primitive neuroectodermal tumor; c) Neuroblastoma; d) Wilms tumor; e) Hepatoblastoma; f) Embryonal Rhabdomyosarcoma; g) Medulloblastoma; h) Pineoblastoma; i) Retinoblastoma; j) Central Nervous System primitive neuroectodermal tumor; k) Neuroepithelioma; l) Desmoplastic small round cell tumor. Read More

Meeting name: SPR 2022 Annual Meeting & Postgraduate Course , 2022

Authors: Defendi Larissa De Andrade, Balancin Marcelo, Tostes Rodrigo De Oliveira, Rodriguez Larry Marden Rabindranath Alpaca, Regacini Rodrigo, Lederman Henrique

Keywords: Small Round Blue Cell Tumors

Computed Tomography (CT) is still recommended as the first-line imaging method for the evaluation of premature closure of cranial sutures. The aims of this exhibit are: 1. To present the anatomy and physiology of cranial sutures; 2. To discuss technical aspects of CT imaging and structured report in craniosynostosis; 3. To present the main imaging findings of isolated and syndromic craniosynostosis. Teaching cases from our institution will be employed to illustrate the following topics: 1. Cranial sutures: anatomy and time of closure; 2. Imaging evaluation of cranial sutures: sonography (US), radiograph (XR) and CT - technique and protocols; 3. Recognizing a patent suture and distinguishing a normally closed suture from synostosis; 4. Craniosynostosis: pathophysiology, clinical features and associated genetic conditions; 5. Multi-modality imaging appearance of: - Dolichocephaly; - Brachycephaly; - Trigonocephaly; - Posterior plagiocephaly. 6. The role of imaging in evaluating positional plagiocephaly 7. Syndromic craniosynostosis - main CT imaging features of: - Crouzon syndrome - Apert syndrome - Pfeiffer syndrome - Saethre-Chotzen Syndrome 8. What matters for surgery planning? Tips on how to organize your report. Read More

Meeting name: SPR 2022 Annual Meeting & Postgraduate Course , 2022

Authors: Defendi Larissa De Andrade, Sbardelotto Monique, Rodriguez Larry Marden Rabindranath Alpaca, Tostes Rodrigo De Oliveira, Camargo Marcos, Monteiro Soraya, Regacini Rodrigo

Keywords: Craniosynostosis