Klippel-Trenaunay Syndrome (KTS) is a rare cutaneous vascular malformation syndrome involving capillary, venous, and lymphatic malformations often involving a unilateral lower limb. Patients with KTS can also have disease involvement of the gastrointestinal (GI) tract, predisoposing patients to GI bleeding. Here, we present a case of a 15-year-old male with known congenital Klippel-Trenaunay Syndrome involving the left lower extremity presenting with acutely worsening rectal bleeding. The patient presented with two weeks of rectal bleeding, fatigue, and weakness. On initial evaluation, the patient was found to have acute drop in hemoglobin concerning for active GI bleeding. Initial imaging included a tagged red blood cell scan, which demonstrated diffuse increased radiotracer activity along the left hemiabdomen, consistent with active bleed. However, the etiology/source of bleeding at this time could not be determined due to the extensive abdominal involvement. Further evaluation included CT angiography of the abdomen and pelvis, which revealed a large, extensive venous malformation extending throughout the wall of the descending and rectosigmoid colon, with venous malformation extending throughout the left lateral pelvic musculature. Arterial phase imaging demonstrated abnormal enhancement of the mucosa of the descending and rectosigmoid colon, and venous phase imaging demonstrated contrast blushing throughout the descending colon concerning for active bleeding, without clear identifiable source. Due to decline in clinical status and refractory anemia requiring massive transfusion, the patient was evaluated surgically and subsequently underwent emergent colectomy and left lower quadrant ostomy placement. Intraoperative findings demonstrated a massively dilated sigmoid colon with complex tangle of cavernous venous malformations involving approximately two feet of bowel. In setting of a technically challenging operation, the patient’s post-operative course has been complicated by rectal stump dehiscence, multiple pelvic abscesses, and guarded prognosis. In summary, KTS is a rare syndrome involving extensive capillary, lymphatic, and venous malformations, with gastrointestinal involvement predisposing patients to potential life-threating GI bleeding. Here we review a case of a 15-year-old male with KTS presenting with refractory GI bleeding in an extensive colonic vascular malformation necessitating emergent colectomy. Read More

Meeting name: SPR 2025 Annual Meeting , 2025

Authors: Stecher Priscilla, Ordonez Alvaro, Noor Abass

Keywords: Klippel-Trenaunay Syndrome, Venous Malformation, Rectal Bleeding

Bilateral renal masses in children are uncommon but can have stakes. Entities such as nephrogenic rests and nephroblastomatosis, bilateral Wilms tumor (Stage V), hereditary renal cell carcinoma associated with von Hippel Lindau and tuberous sclerosis, DICER1 related cystic neoplasms, and lymphoma often overlap in appearance on imaging. Management pathways can differ widely and can range from surveillance to more aggressive surgical managements. Therefore, radiologists need to integrate imaging findings with clinical and genetic clues to protect renal function and optimize outcomes This exhibit is designed to help participants recognize multimodality imaging features of uncommon bilateral renal masses beyond simple cysts, angiomyolipomas, infection, and metastases. It also highlights key syndromic associations and epidemiology, including WAGR, Denys Drash, Beckwith Wiedemann, von Hippel Lindau, tuberous sclerosis, and DICER1. Finally, it presents a structured, stepwise framework for refining the differential. It guides recommendations for next steps, such as surveillance, biopsy, or chemotherapy first. The approach emphasizes nephron preservation and close collaboration across the care team. Read More

Meeting name: IPR 2026 Congress , 2026

Authors: Tabor Biniyam Beyene, Belachew Bethelhem, Noor Abass

Keywords: Renal Lesions, Pediatric

To understand the current state of pediatric IR in Ethiopia, recognize the barriers limiting its establishment, and explore a context-specific roadmap for establishing a sustainable practice that ensures equitable access to minimally invasive care for children in the country. Ethiopia is the second most populous country in Africa, and 39.1% of the population is between 0 and 14 years of age. Tikur Anbessa Specialized Hospital, Ethiopia’s largest teaching and referral hospital, serves approximately 500,000 patients annually, of whom 48% are children. In 2008, its radiology department partnered with the Children’s Hospital of Philadelphia to establish Ethiopia’s first pediatric radiology fellowship program, which has successfully trained subspecialists and integrated basic image-guided procedures. However, there is currently no established pediatric interventional radiology training program in the country. Read More

Meeting name: IPR 2026 Congress , 2026

Authors: Hailu Samuel Sisay, Noor Abass, Darge Kassa

Keywords: Global Health, Interventional, Educational Intervention