OEIS complex is the most severe end of the expectrum of the exstrophy - epispadias complex . It is characterized by omphalocele, extrophy, imperforate anus and spinal defects and is often associated with other malformations on chest, abdomen genitourinary, skeletal and neurologic. The incidence of OEIS complex is very rare, estimated to occur in 0, 5 – 1 per 200 000 live births. We present a case of OEIS complex associated with horseshoe kidney. The baby was delivered by vaginal delivery (GA 39 weeks). Present normal male kariotype. On physical examination there were omphalocele with herniation of a segment of the large bowel, cloacal exstrophy with two hemi bladders, imperforate anus and spina bifida. No external genitalia were identified on physical examination but bilateral cryptorchidism was observed in pelvic MRI Renal ultrasound show hoershoe kidney with left pelvic ectasia that was confirmed on abdominal MRI and urotomography. Spinal ultrasound and MRI show lipomyelomenigocele and low spinal cord insertion. Also the baby has sacral segmentation defects and congenital hip subluxation. Read More

Meeting name: IPR 2016 Conjoint Meeting & Exhibition , 2016

Authors: Matos Rojas Irma, Katekaru Tokeshi Doris

Keywords: OEIS complex, horseshoe kidney, extrophy - epispadias complex, magnetic resonance imaging, ultrasound

We report a case of a term neonate who shortly after birth developed respiratory distress and left-sided pneumothorax. The pneumothorax was drained by a chest tube and the patient was referred to our institution. On day 17 of life a chest Xray and chest CT were performed demonstrating a multiloculated cystic lesion compromising the left upper lobe, most likely representing congenital pulmonary airway malformation (CPAM) type II (Figure 1). No abnormal systemic vessels were identified. At that time the patient was diagnosed with B influenza infection and the surgical intervention was deferred. Over the next several days the patient demonstrated improvement of the respiratory distress and progressive decrease of supplementary oxygen need. On day 25 of life the patient presented significant clinical improvement and, at physical examination, breath sounds were found on the left hemithorax. A follow-up chest xray demonstrated spontaneous resolution of the prior visualized cystic lesion that was confirmed with a chest CT (Figure 2). Postnatal spontaneous resolution of CPAM have been reported in only few cases, with resolution of the malformation in few months or years. Although we do not have pathologic confirmation, we postulate that our case represent CPAM type II that resolved spontaneously before the first month of life. The management of CPAM diagnosed during the neonatal period remains controversial, some authors recommend postpone surgical intervention in asymptomatic neonates and in patients with prompt resolution of respiratory distress without other significant anomalies. Our case illustrates the possibility of spontaneous resolution of CPAM and adds to the few reported cases that recommend conservative treatment. Read More

Meeting name: IPR 2016 Conjoint Meeting & Exhibition , 2016

Authors: Valdez Quintana Melissa, Ugas Carlos, Katekaru Tokeshi Doris, Matos Rojas Irma, Delgado Edgar

Keywords: CPAM, spontaneous resolution, neonate, CT

Significant progress in improving outcome for patients with oncohematological diseases are attributed to intensive chemotherapy, bone marrow transplantation, platelet transfusions, development of new imaging techniques, new antimicrobials and others. All these advances increase the survival of these patients which in turn increases the frequent of risk of infections that are substantial cause of morbidity and mortality in these patients. The purpose of this exhibit is to show the spectrum of infections in these patients; describe the imaging finding according to the etiology and associated factors. There are a number of factors that need to be considered in order to interpret abnormalities seen on radiology as the type of hematological disease, stage of the hematological disease, treatment phase, profile of immunodeficiency, treatment for infection received, patient history and clinical signs. For example, according to type of immunosuppression there are different spectrum of infections but leukemia affect all types of immunosuppression that include neutropenia, T cell defect and B cell defect. Read More

Meeting name: IPR 2016 Conjoint Meeting & Exhibition , 2016

Authors: Matos Rojas Irma, Lazarte Claudia, Katekaru Tokeshi Doris, Ugas Carlos, Valdez Quintana Melissa, Casamayor Alvina

Keywords: infections, Hematologic malignancy, Pediatric, diagnostic accuracy, aplastic anemia

The purpose of this exhibit is to review imagings findings of anomalous pulmonary venous return on angiotomography and describe anomalies associated. Magnetic resonance (MR) imaging and computed tomography (CT) are used in diagnostic and follow – up the congenital vein anomalies. CT provides superior spatial resolution and short time but there is exposure to ionizing radiation. However in many hospital there are only the possibility of obtain CT imaging in neonates and infant. The total anomalous pulmonary venous return (TAPVR) is the result of failure of the common pulmonary vein to connect to the left atrium with persistence of the primitive splanchnic connections of the pulmonary veins. There are four categories: supracardiac, cardiac, infracardiac and mixed. The partial anomalous pulmonary venous return (PAPVR) occurs when some but not all segments of the developing lung failed to establish connections with the common pulmonary vein. Read More

Meeting name: IPR 2016 Conjoint Meeting & Exhibition , 2016

Authors: Matos Rojas Irma, Ugas Carlos, Megue Huamani Marlin, Katekaru Tokeshi Doris, Lazarte Claudia, Valdez Quintana Melissa, Alpaca Rodriguez Larry, Casamayor Alvina

Keywords: anomalous pulmonary venous return, pulmonary veins, CT Scan