Trout Andrew,  Dillman Jonathan,  Alsaied Tarek,  Lubert Adam,  Palermo Joseph,  Lorts Angela,  Khoury Philip

Final Pr. ID: Paper #: 039

The Fontan operation, used to palliate single ventricle congenital heart disease, increases venous pressure in the liver and is associated with Fontan associated liver disease (FALD), for which liver fibrosis is the final common pathway. Elastography (ultrasound [US] or MRI) can be used to non-invasively measure liver stiffness associated with liver fibrosis. However, these measures are confounded in Fontan patients due to venous congestion. The purpose of this study was to prospectively document the stiffening effect of passive hepatic congestion following the Fontan operation and track changes in liver stiffness over the post-operative period. Read More

Authors:  Trout Andrew,  Dillman Jonathan,  Alsaied Tarek,  Lubert Adam,  Palermo Joseph,  Lorts Angela,  Khoury Philip

Keywords:  Fontan ,  Liver ,  Ultrasound

Fujiwara Takashi,  Browne Lorna,  Malone Ladonna,  Lu Quin,  Fonseca Brian,  Dimaria Michael,  Barker Alex

Final Pr. ID: Paper #: 040

4D flow MRI with full coverage of the heart and proximal vessels is a powerful tool to understand hemodynamic pathology arising from congenital heart disease (CHD) and subsequent surgery; however, scan times often exceed 10 minutes thereby limiting widespread adoption in pediatrics. Decreasing scan time using compressed-SENSE (CS), a combination of conventional parallel imaging (SENSE) and randomized spatial undersampling, shows promise over SENSE alone. However, both the feasibility and its effect on accurate flow quantification in pediatrics has not been evaluated. This study investigated the feasibility of CS for pediatric 4D flow MRI to quantify flow indices used in risk stratification of CHD such as coarctation or pulmonary regurgitation, in comparison with SENSE. Read More

Authors:  Fujiwara Takashi,  Browne Lorna,  Malone Ladonna,  Lu Quin,  Fonseca Brian,  Dimaria Michael,  Barker Alex

Keywords:  4D flow ,  Compressed SENSE ,  Congenital heart disease

Naresh Nivedita,  Browne Lorna,  Barker Alex,  Malone Ladonna,  Fujiwara Takashi,  Hulseberg-dwyer Emma,  Mcgee Janet,  Lu Quin,  Twite Mark,  Dimaria Michael,  Fonseca Brian

Final Pr. ID: Paper #: 041

Introduction: Conventional pediatric MRI acquisitions of a short axis (SA) stack for ventricular volumes typically requires one breath-hold per slice, resulting in multiple coordinated breath-holds under anesthesia to acquire the entire stack. Here, we aim to validate a compressed sensing approach to reduce breath-holding during SA balanced steady state free precession (bSSFP) cine imaging. Equivalency is tested via qualitative image scoring and global volumes compared to conventional bSSFP cine imaging. Read More

Authors:  Naresh Nivedita,  Browne Lorna,  Barker Alex,  Malone Ladonna,  Fujiwara Takashi,  Hulseberg-dwyer Emma,  Mcgee Janet,  Lu Quin,  Twite Mark,  Dimaria Michael,  Fonseca Brian

Keywords:  Compressed Sensing ,  Cardiac Function ,  Anesthesia

Ugas Charcape Carlos,  Nicho-póvez Minorka,  Pacheco-cárdenas Claudia,  Palomino-alfaro Liz,  Barrera Christian,  Otero Hansel

Final Pr. ID: Paper #: 042

To describe CTA findings of children with left pulmonary artery sling (LPA) using the classification proposed by Wells, et al and report associated anomalies and surgical outcomes. Read More

Authors:  Ugas Charcape Carlos,  Nicho-póvez Minorka,  Pacheco-cárdenas Claudia,  Palomino-alfaro Liz,  Barrera Christian,  Otero Hansel

Keywords:  pulmonary artery sling ,  children ,  ct

Hatoum Hoda,  Krishnamurthy Rajesh,  Parthasarathy Jayanthi,  Flemister Dorma,  Mery Carlos,  Molossi Silvana,  Dasi Lakshmi Prasad

Final Pr. ID: Paper #: 043

AAOCA is the second leading cause of sudden cardiac death in the young which typically occurs with exertion. With in-vitro patient-specific modeling the study aims to assess the differences in fractional flow reserve(FFR)with hyperemia(high-flow)in a patient with AAOCA with a confirmed ischemic event and compare it to a patient with normal coronaries Read More

Authors:  Hatoum Hoda,  Krishnamurthy Rajesh,  Parthasarathy Jayanthi,  Flemister Dorma,  Mery Carlos,  Molossi Silvana,  Dasi Lakshmi Prasad

Keywords:  Aaoca ,  CT ,  Coronary

Parthasarathy Jayanthi,  Hatoum Hoda,  Flemister Dorma,  Mery Carlos,  Molossi Silvana,  Dasi Lakshmi Prasad,  Krishnamurthy Rajesh

Final Pr. ID: Paper #: 044

Morphological features including intramural course, high ostial location, and slit-like ostium are considered risk factors for sudden death in patients with AAOCA. Assessment of coronary blood flow at rest and hyperemia may contribute to understanding the cause of death, and to risk stratification and management. A patient-specific biomechanical 3D printed model incorporating morphological features derived from CTA was developed to quantify coronary blood flow in AAOCA. Read More

Authors:  Parthasarathy Jayanthi,  Hatoum Hoda,  Flemister Dorma,  Mery Carlos,  Molossi Silvana,  Dasi Lakshmi Prasad,  Krishnamurthy Rajesh

Keywords:  Anomalous coronary ,  3D Printing ,  FFR

Diaz Eric,  Hor Kan,  Krishnamurthy Ramkumar,  Lee Simon,  Krishnamurthy Rajesh

Final Pr. ID: Paper #: 045

DMD is X-linked cardiac and skeletal myopathy caused by dystrophin protein deficiency with early death by cardiomyopathy. Cardiac magnetic resonance imaging (CMR) with myocardial fibrosis by late gadolinium enhancement (LGE) precedes decline in ejection fraction (LVEF) and may alter management in DMD. Muscle weakness limits ability to perform consistent breath-hold (BH) in traditional LGE sequences. Free-breathing (FB) LGE with motion correction (MOCO) allows improved visualization. We hypothesize that FB LGE with MOCO provides equivalent diagnostic quality with similar scan time to traditional LGE sequence. Read More

Authors:  Diaz Eric,  Hor Kan,  Krishnamurthy Ramkumar,  Lee Simon,  Krishnamurthy Rajesh

Keywords:  LGE ,  MOCO ,  CMR

Zafar Faizeen,  Trout Andrew,  Palermo Joseph,  Alsaied Tarek,  Dillman Jonathan

Final Pr. ID: Paper #: 046

Portal hypertension is a manifestation of Fontan-related venous congestion and hepatic fibrosis. We studied the prevalence of radiologic evidence of portal hypertension (RP) and its association with Fontan hemodynamics and adverse outcomes. We also tested the validity of the VAST score, used in a prior study, in our population. Read More

Authors:  Zafar Faizeen,  Trout Andrew,  Palermo Joseph,  Alsaied Tarek,  Dillman Jonathan

Keywords:  Fontan ,  Portal Hypertension ,  Congenital Heart Disease

Salman Rida,  More Snehal,  Ferreira Botelho Marcos,  Ketwaroo Pamela,  Masand Prakash,  Molossi Silvana,  Jadhav Siddharth

Final Pr. ID: Paper #: 047

Anomalous Aortic Origin of Coronary Artery (AAOCA) is the 2nd most common cause of sudden cardiac death in the young. Coronary artery origins are evaluated as part of transthoracic echocardiography (TTE) and diagnostic precision may be limited by technical limitations, operator dependence, and patient cooperation. MRI and gated Cardiac Computed Tomographic Angiography (CCTA) are often utilized in patients where an anomaly is suspected on TTE. There is limited literature comparing TTE and CCTA in children with suspected AAOCA. The purpose of this study is to determine the distribution of various coronary anomalies comparing TTE and CCTA data, and define the added value advanced imaging brings in clinical decision-making. Read More

Authors:  Salman Rida,  More Snehal,  Ferreira Botelho Marcos,  Ketwaroo Pamela,  Masand Prakash,  Molossi Silvana,  Jadhav Siddharth

Keywords:  Anomalous coronaries ,  CT angiography ,  Echocardiography

Salman Rida,  More Snehal,  Ferreira Botelho Marcos,  Ketwaroo Pamela,  Masand Prakash,  Jadhav Siddharth

Final Pr. ID: Paper #: 048

Norwood procedure is a 3-stage surgical palliation for patients with functionally single ventricle anatomy, most commonly hypoplastic left heart syndrome. Complications after stage I operation are not uncommon and include Blalock Taussig Thomas (BTT) /Sano shunt abnormalities, Damus-Kaye-Stansel (DKS) anastomotic narrowing, and neo-aortic arch /branch vessel stenosis. Transthoracic echocardiography (TTE) is traditionally the mainstay for evaluation. The purpose of our study is to compare Gated Cardiac Computed Tomographic Angiography (CCTA) with TTE when evaluating post-operative complications after stage I Norwood procedure and implications of CCTA findings on management.
Read More

Authors:  Salman Rida,  More Snehal,  Ferreira Botelho Marcos,  Ketwaroo Pamela,  Masand Prakash,  Jadhav Siddharth

Keywords:  Congenital heart disease ,  CT Angiography ,  Echocardiography